Hepato-Lenticular Degeneration

The absorption and excretion of radiocopper in hepato-lenticular degeneration (Wilson's disease).

Tapetoretinal degeneration in the cerebro-hepato-renal (Zellweger's) syndrome.

Electrophysiological and histopathological study of a baby suffering from Zellweger's syndrome and presenting progressive retinal dysfunction showed this to be related to degenerative changes in the photoreceptor cells and pigment epithelium and to defective myelination of the optic nerve. Disturbances of bile acid and lysine metabolism were also demonstrated, lending support to the concept tha...

High Maneuverability Lenticular Airship

This paper presents and describes a new lenticular shaped airship that allows 3D omnidirectional movements. The airship is intended to be part of a cooperative aerial system based in the synergy between an airship and a group of micro-quad rotors capable of long time missions as environmental, biodiversity monitoring, WiSAR missions, road monitoring, detection of forest fires, etc. The emphasis...

Lenticular abnormalities in children.

PURPOSE To study the lenticular problems in children presenting at an apex institute. METHODS Retrospective analysis of records (< 14 years) of new lens clinic cases was done. RESULTS Of 1,047 children, 687 were males. Mean age at presentation was 6.35 ± 4.13 years. Developmental cataract was seen in 45.6% and posttraumatic cataract in 29.7% of patients. Other abnormalities were cataract wi...

Hiperqueratose lenticular persistente

Flegel's disea se, also known as hyper ke ra to sis len ti cu la ris pers tans, is a rare skin disea se cha rac te ri zed by small red dish-brown asympto ma tic hyper ke ra to tic papu les usually loca ted on the lower extre mi ties. The his to pa tho lo gi cal fea tu res are hype ror tho ke ra to sis, epi der mal atrophy and band-like inflam ma tory infil tra te in the super fi cial der mis. T...